Abstract: Extraadrenal paragangliomas are tumors composed of neuroendocrine-derived, catecholamine-secreting chromaffin cells inducing hypertension, palpitations, and diaphoresis [1]. Although extraadrenal paragangliomas are found in a variety of anatomic sites that normally host paraganglia—from the carotid body to the abdominal paraaortic region—the bladder is an uncommon location for paragangliomas. Bladder paragangliomas represent approximately 6% of extraadrenal paragangliomas and only 0.05% of all bladder tumors [2,3]. We present a rare case of primary paraganglioma affecting the bladder dome.
. [J]. Asian Journal of Urology, 2022, 9(1): 94-96.
Sagar Patel, Judy Hamad, Matthew E. Nielsen, Steven Johnson. Management and evaluation of bladder paragangliomas. Asian Journal of Urology, 2022, 9(1): 94-96.
Ranaweera M, Chung E. Bladder paraganglioma: A report of case series and critical review of current literature. World J Clin Cases 2014; 2:591e5.
[2]
Lee KY, Oh Y-W, Noh HJ, Lee YJ, Yong H-S, Kang E-Y, et al. Extraadrenal paragangliomas of the body: Imaging features. AJR Am J Roentgenol 2006; 187:492e504.
[3]
Priyadarshi V, Pal DK. Paraganglioma of urinary bladder. Urol Ann 2015; 7:402e4.
[4]
Sonmez G, Tombul ST, Golbasi A, Demirtas T, Akgun H, Demirtas A. Symptomatic paraganglioma of the urinary bladder: A rare case treated with a combined surgical approach. Urol Case Rep 2020; 33:101290. https://doi.org/10.1016/j.eucr.2020.101290.
[5]
Martucci VL, Lorenzo ZG, Weintraub M, del Rivero J, Ling A, Merino M, et al. Association of urinary bladder paragangliomas with germline mutations in the SDHB and VHL genes. Urol Oncol 2015; 33:167. https://doi.org/10.1016/j.urolonc.2014.11.017.e13e20.
[6]
Li H, Xie J, Chen Z, Yang S, Lai Y. Diagnosis and treatment of a rare tumor-bladder paraganglioma. Mol Clin Oncol 2020; 13:40. https://doi.org/10.3892/mco.2020.2110.